Massive spinal–ischial dysplasia and extensive spinal dyssygmentation in a Tunisian child with severe form of Cleido- cranial dysplasia
نویسندگان
چکیده
Kyphoscoliosis is a complication of some bone dysplasias, including Cleido-cranial dysplasia (CCD). We report on massive spinal dysplasia secondary to severe spinal dyssygmentation associated with marked defective ossification of the ischium, detected in a Tunisian female child with a severe form of Cleido-cranial dysplasia. Literature review on Cleido cranial dysplasia and associated spinal abnormalities showed no previous similar reports as encountered in our patient.
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